Severe Refractory Anemia in Primary Intestinal Lymphangiectasia. A Case Report.
Identifieur interne : 001841 ( Main/Exploration ); précédent : 001840; suivant : 001842Severe Refractory Anemia in Primary Intestinal Lymphangiectasia. A Case Report.
Auteurs : Vasile Daniel Balaban [Roumanie] ; Alina Popp [Finlande] ; Mugur Grasu [Roumanie] ; Florina Vasilescu [Roumanie] ; Mariana Jinga [Roumanie]Source :
- Journal of gastrointestinal and liver diseases : JGLD [ 1842-1121 ] ; 2015.
Descripteurs français
- KwdFr :
- Antifibrinolytiques (usage thérapeutique), Anémie (), Anémie (diagnostic), Anémie (sang), Anémie (étiologie), Biopsie, Compléments alimentaires, Embolisation thérapeutique, Endoscopie gastrointestinale, Entéropathie exsudative (), Entéropathie exsudative (étiologie), Humains, Indice de gravité médicale, Jeune adulte, Lymphangiectasie intestinale (), Lymphangiectasie intestinale (diagnostic), Lymphoedème (), Lymphoedème (diagnostic), Maladie chronique, Mâle, Octréotide (usage thérapeutique), Procédures de chirurgie digestive, Régime pauvre en graisses, Résultat thérapeutique, Triglycéride (administration et posologie).
- MESH :
- administration et posologie : Triglycéride.
- diagnostic : Anémie, Lymphangiectasie intestinale, Lymphoedème.
- sang : Anémie.
- usage thérapeutique : Antifibrinolytiques, Octréotide.
- étiologie : Anémie, Entéropathie exsudative.
- Anémie, Biopsie, Compléments alimentaires, Embolisation thérapeutique, Endoscopie gastrointestinale, Entéropathie exsudative, Humains, Indice de gravité médicale, Jeune adulte, Lymphangiectasie intestinale, Lymphoedème, Maladie chronique, Mâle, Procédures de chirurgie digestive, Régime pauvre en graisses, Résultat thérapeutique.
English descriptors
- KwdEn :
- Anemia (blood), Anemia (diagnosis), Anemia (etiology), Anemia (therapy), Antifibrinolytic Agents (therapeutic use), Biopsy, Chronic Disease, Diet, Fat-Restricted, Dietary Supplements, Digestive System Surgical Procedures, Embolization, Therapeutic, Endoscopy, Gastrointestinal, Humans, Lymphangiectasis, Intestinal (complications), Lymphangiectasis, Intestinal (diagnosis), Lymphangiectasis, Intestinal (therapy), Lymphedema (complications), Lymphedema (diagnosis), Lymphedema (therapy), Male, Octreotide (therapeutic use), Protein-Losing Enteropathies (etiology), Protein-Losing Enteropathies (therapy), Severity of Illness Index, Treatment Outcome, Triglycerides (administration & dosage), Young Adult.
- MESH :
- chemical , administration & dosage : Triglycerides.
- chemical , therapeutic use : Antifibrinolytic Agents, Octreotide.
- blood : Anemia.
- complications : Lymphangiectasis, Intestinal, Lymphedema.
- diagnosis : Anemia, Lymphangiectasis, Intestinal, Lymphedema.
- etiology : Anemia, Protein-Losing Enteropathies.
- therapy : Anemia, Lymphangiectasis, Intestinal, Lymphedema, Protein-Losing Enteropathies.
- Biopsy, Chronic Disease, Diet, Fat-Restricted, Dietary Supplements, Digestive System Surgical Procedures, Embolization, Therapeutic, Endoscopy, Gastrointestinal, Humans, Male, Severity of Illness Index, Treatment Outcome, Young Adult.
Abstract
Primary intestinal lymphangiectasia (Waldmann's disease) is a rare disease characterized by dilated lymphatics in the small bowel leading to an exudative enteropathy with lymphopenia, hypoalbuminemia and hypogammaglobulinemia.
PubMed: 26405709
Affiliations:
Links toward previous steps (curation, corpus...)
- to stream PubMed, to step Corpus: 000C22
- to stream PubMed, to step Curation: 000C22
- to stream PubMed, to step Checkpoint: 000C22
- to stream Ncbi, to step Merge: 007936
- to stream Ncbi, to step Curation: 007936
- to stream Ncbi, to step Checkpoint: 007936
- to stream Main, to step Merge: 001843
- to stream Main, to step Curation: 001841
Le document en format XML
<record><TEI><teiHeader><fileDesc><titleStmt><title xml:lang="en">Severe Refractory Anemia in Primary Intestinal Lymphangiectasia. A Case Report.</title>
<author><name sortKey="Balaban, Vasile Daniel" sort="Balaban, Vasile Daniel" uniqKey="Balaban V" first="Vasile Daniel" last="Balaban">Vasile Daniel Balaban</name>
<affiliation wicri:level="1"><nlm:affiliation>Dr. Carol Davila Central Military Emergency University Hospital; Carol Davila University of Medicine and Pharmacy, Bucharest, Romania.</nlm:affiliation>
<country xml:lang="fr">Roumanie</country>
<wicri:regionArea>Dr. Carol Davila Central Military Emergency University Hospital; Carol Davila University of Medicine and Pharmacy, Bucharest</wicri:regionArea>
<wicri:noRegion>Bucharest</wicri:noRegion>
</affiliation>
</author>
<author><name sortKey="Popp, Alina" sort="Popp, Alina" uniqKey="Popp A" first="Alina" last="Popp">Alina Popp</name>
<affiliation wicri:level="1"><nlm:affiliation>Carol Davila University of Medicine and Pharmacy; Alfred Rusescu Institute for Mother and Child Care, Bucharest, Romania; Tampere Center for Child Health Research, University of Tampere and Tampere University Hospital, Finland. alina.popp@uta.fi.</nlm:affiliation>
<country xml:lang="fr">Finlande</country>
<wicri:regionArea>Carol Davila University of Medicine and Pharmacy; Alfred Rusescu Institute for Mother and Child Care, Bucharest, Romania; Tampere Center for Child Health Research, University of Tampere and Tampere University Hospital</wicri:regionArea>
<wicri:noRegion>University of Tampere and Tampere University Hospital</wicri:noRegion>
</affiliation>
</author>
<author><name sortKey="Grasu, Mugur" sort="Grasu, Mugur" uniqKey="Grasu M" first="Mugur" last="Grasu">Mugur Grasu</name>
<affiliation wicri:level="1"><nlm:affiliation>Fundeni Clinical Institute, Bucharest, Romania.</nlm:affiliation>
<country xml:lang="fr">Roumanie</country>
<wicri:regionArea>Fundeni Clinical Institute, Bucharest</wicri:regionArea>
<wicri:noRegion>Bucharest</wicri:noRegion>
</affiliation>
</author>
<author><name sortKey="Vasilescu, Florina" sort="Vasilescu, Florina" uniqKey="Vasilescu F" first="Florina" last="Vasilescu">Florina Vasilescu</name>
<affiliation wicri:level="1"><nlm:affiliation>Dr. Carol Davila Central Military Emergency University Hospital, Bucharest, Romania.</nlm:affiliation>
<country xml:lang="fr">Roumanie</country>
<wicri:regionArea>Dr. Carol Davila Central Military Emergency University Hospital, Bucharest</wicri:regionArea>
<wicri:noRegion>Bucharest</wicri:noRegion>
</affiliation>
</author>
<author><name sortKey="Jinga, Mariana" sort="Jinga, Mariana" uniqKey="Jinga M" first="Mariana" last="Jinga">Mariana Jinga</name>
<affiliation wicri:level="1"><nlm:affiliation>Dr. Carol Davila Central Military Emergency University Hospital; Carol Davila University of Medicine and Pharmacy, Bucharest, Romania.</nlm:affiliation>
<country xml:lang="fr">Roumanie</country>
<wicri:regionArea>Dr. Carol Davila Central Military Emergency University Hospital; Carol Davila University of Medicine and Pharmacy, Bucharest</wicri:regionArea>
<wicri:noRegion>Bucharest</wicri:noRegion>
</affiliation>
</author>
</titleStmt>
<publicationStmt><idno type="wicri:source">PubMed</idno>
<date when="2015">2015</date>
<idno type="RBID">pubmed:26405709</idno>
<idno type="pmid">26405709</idno>
<idno type="wicri:Area/PubMed/Corpus">000C22</idno>
<idno type="wicri:explorRef" wicri:stream="PubMed" wicri:step="Corpus" wicri:corpus="PubMed">000C22</idno>
<idno type="wicri:Area/PubMed/Curation">000C22</idno>
<idno type="wicri:explorRef" wicri:stream="PubMed" wicri:step="Curation">000C22</idno>
<idno type="wicri:Area/PubMed/Checkpoint">000C22</idno>
<idno type="wicri:explorRef" wicri:stream="Checkpoint" wicri:step="PubMed">000C22</idno>
<idno type="wicri:Area/Ncbi/Merge">007936</idno>
<idno type="wicri:Area/Ncbi/Curation">007936</idno>
<idno type="wicri:Area/Ncbi/Checkpoint">007936</idno>
<idno type="wicri:Area/Main/Merge">001843</idno>
<idno type="wicri:Area/Main/Curation">001841</idno>
<idno type="wicri:Area/Main/Exploration">001841</idno>
</publicationStmt>
<sourceDesc><biblStruct><analytic><title xml:lang="en">Severe Refractory Anemia in Primary Intestinal Lymphangiectasia. A Case Report.</title>
<author><name sortKey="Balaban, Vasile Daniel" sort="Balaban, Vasile Daniel" uniqKey="Balaban V" first="Vasile Daniel" last="Balaban">Vasile Daniel Balaban</name>
<affiliation wicri:level="1"><nlm:affiliation>Dr. Carol Davila Central Military Emergency University Hospital; Carol Davila University of Medicine and Pharmacy, Bucharest, Romania.</nlm:affiliation>
<country xml:lang="fr">Roumanie</country>
<wicri:regionArea>Dr. Carol Davila Central Military Emergency University Hospital; Carol Davila University of Medicine and Pharmacy, Bucharest</wicri:regionArea>
<wicri:noRegion>Bucharest</wicri:noRegion>
</affiliation>
</author>
<author><name sortKey="Popp, Alina" sort="Popp, Alina" uniqKey="Popp A" first="Alina" last="Popp">Alina Popp</name>
<affiliation wicri:level="1"><nlm:affiliation>Carol Davila University of Medicine and Pharmacy; Alfred Rusescu Institute for Mother and Child Care, Bucharest, Romania; Tampere Center for Child Health Research, University of Tampere and Tampere University Hospital, Finland. alina.popp@uta.fi.</nlm:affiliation>
<country xml:lang="fr">Finlande</country>
<wicri:regionArea>Carol Davila University of Medicine and Pharmacy; Alfred Rusescu Institute for Mother and Child Care, Bucharest, Romania; Tampere Center for Child Health Research, University of Tampere and Tampere University Hospital</wicri:regionArea>
<wicri:noRegion>University of Tampere and Tampere University Hospital</wicri:noRegion>
</affiliation>
</author>
<author><name sortKey="Grasu, Mugur" sort="Grasu, Mugur" uniqKey="Grasu M" first="Mugur" last="Grasu">Mugur Grasu</name>
<affiliation wicri:level="1"><nlm:affiliation>Fundeni Clinical Institute, Bucharest, Romania.</nlm:affiliation>
<country xml:lang="fr">Roumanie</country>
<wicri:regionArea>Fundeni Clinical Institute, Bucharest</wicri:regionArea>
<wicri:noRegion>Bucharest</wicri:noRegion>
</affiliation>
</author>
<author><name sortKey="Vasilescu, Florina" sort="Vasilescu, Florina" uniqKey="Vasilescu F" first="Florina" last="Vasilescu">Florina Vasilescu</name>
<affiliation wicri:level="1"><nlm:affiliation>Dr. Carol Davila Central Military Emergency University Hospital, Bucharest, Romania.</nlm:affiliation>
<country xml:lang="fr">Roumanie</country>
<wicri:regionArea>Dr. Carol Davila Central Military Emergency University Hospital, Bucharest</wicri:regionArea>
<wicri:noRegion>Bucharest</wicri:noRegion>
</affiliation>
</author>
<author><name sortKey="Jinga, Mariana" sort="Jinga, Mariana" uniqKey="Jinga M" first="Mariana" last="Jinga">Mariana Jinga</name>
<affiliation wicri:level="1"><nlm:affiliation>Dr. Carol Davila Central Military Emergency University Hospital; Carol Davila University of Medicine and Pharmacy, Bucharest, Romania.</nlm:affiliation>
<country xml:lang="fr">Roumanie</country>
<wicri:regionArea>Dr. Carol Davila Central Military Emergency University Hospital; Carol Davila University of Medicine and Pharmacy, Bucharest</wicri:regionArea>
<wicri:noRegion>Bucharest</wicri:noRegion>
</affiliation>
</author>
</analytic>
<series><title level="j">Journal of gastrointestinal and liver diseases : JGLD</title>
<idno type="eISSN">1842-1121</idno>
<imprint><date when="2015" type="published">2015</date>
</imprint>
</series>
</biblStruct>
</sourceDesc>
</fileDesc>
<profileDesc><textClass><keywords scheme="KwdEn" xml:lang="en"><term>Anemia (blood)</term>
<term>Anemia (diagnosis)</term>
<term>Anemia (etiology)</term>
<term>Anemia (therapy)</term>
<term>Antifibrinolytic Agents (therapeutic use)</term>
<term>Biopsy</term>
<term>Chronic Disease</term>
<term>Diet, Fat-Restricted</term>
<term>Dietary Supplements</term>
<term>Digestive System Surgical Procedures</term>
<term>Embolization, Therapeutic</term>
<term>Endoscopy, Gastrointestinal</term>
<term>Humans</term>
<term>Lymphangiectasis, Intestinal (complications)</term>
<term>Lymphangiectasis, Intestinal (diagnosis)</term>
<term>Lymphangiectasis, Intestinal (therapy)</term>
<term>Lymphedema (complications)</term>
<term>Lymphedema (diagnosis)</term>
<term>Lymphedema (therapy)</term>
<term>Male</term>
<term>Octreotide (therapeutic use)</term>
<term>Protein-Losing Enteropathies (etiology)</term>
<term>Protein-Losing Enteropathies (therapy)</term>
<term>Severity of Illness Index</term>
<term>Treatment Outcome</term>
<term>Triglycerides (administration & dosage)</term>
<term>Young Adult</term>
</keywords>
<keywords scheme="KwdFr" xml:lang="fr"><term>Antifibrinolytiques (usage thérapeutique)</term>
<term>Anémie ()</term>
<term>Anémie (diagnostic)</term>
<term>Anémie (sang)</term>
<term>Anémie (étiologie)</term>
<term>Biopsie</term>
<term>Compléments alimentaires</term>
<term>Embolisation thérapeutique</term>
<term>Endoscopie gastrointestinale</term>
<term>Entéropathie exsudative ()</term>
<term>Entéropathie exsudative (étiologie)</term>
<term>Humains</term>
<term>Indice de gravité médicale</term>
<term>Jeune adulte</term>
<term>Lymphangiectasie intestinale ()</term>
<term>Lymphangiectasie intestinale (diagnostic)</term>
<term>Lymphoedème ()</term>
<term>Lymphoedème (diagnostic)</term>
<term>Maladie chronique</term>
<term>Mâle</term>
<term>Octréotide (usage thérapeutique)</term>
<term>Procédures de chirurgie digestive</term>
<term>Régime pauvre en graisses</term>
<term>Résultat thérapeutique</term>
<term>Triglycéride (administration et posologie)</term>
</keywords>
<keywords scheme="MESH" type="chemical" qualifier="administration & dosage" xml:lang="en"><term>Triglycerides</term>
</keywords>
<keywords scheme="MESH" type="chemical" qualifier="therapeutic use" xml:lang="en"><term>Antifibrinolytic Agents</term>
<term>Octreotide</term>
</keywords>
<keywords scheme="MESH" qualifier="administration et posologie" xml:lang="fr"><term>Triglycéride</term>
</keywords>
<keywords scheme="MESH" qualifier="blood" xml:lang="en"><term>Anemia</term>
</keywords>
<keywords scheme="MESH" qualifier="complications" xml:lang="en"><term>Lymphangiectasis, Intestinal</term>
<term>Lymphedema</term>
</keywords>
<keywords scheme="MESH" qualifier="diagnosis" xml:lang="en"><term>Anemia</term>
<term>Lymphangiectasis, Intestinal</term>
<term>Lymphedema</term>
</keywords>
<keywords scheme="MESH" qualifier="diagnostic" xml:lang="fr"><term>Anémie</term>
<term>Lymphangiectasie intestinale</term>
<term>Lymphoedème</term>
</keywords>
<keywords scheme="MESH" qualifier="etiology" xml:lang="en"><term>Anemia</term>
<term>Protein-Losing Enteropathies</term>
</keywords>
<keywords scheme="MESH" qualifier="sang" xml:lang="fr"><term>Anémie</term>
</keywords>
<keywords scheme="MESH" qualifier="therapy" xml:lang="en"><term>Anemia</term>
<term>Lymphangiectasis, Intestinal</term>
<term>Lymphedema</term>
<term>Protein-Losing Enteropathies</term>
</keywords>
<keywords scheme="MESH" qualifier="usage thérapeutique" xml:lang="fr"><term>Antifibrinolytiques</term>
<term>Octréotide</term>
</keywords>
<keywords scheme="MESH" qualifier="étiologie" xml:lang="fr"><term>Anémie</term>
<term>Entéropathie exsudative</term>
</keywords>
<keywords scheme="MESH" xml:lang="en"><term>Biopsy</term>
<term>Chronic Disease</term>
<term>Diet, Fat-Restricted</term>
<term>Dietary Supplements</term>
<term>Digestive System Surgical Procedures</term>
<term>Embolization, Therapeutic</term>
<term>Endoscopy, Gastrointestinal</term>
<term>Humans</term>
<term>Male</term>
<term>Severity of Illness Index</term>
<term>Treatment Outcome</term>
<term>Young Adult</term>
</keywords>
<keywords scheme="MESH" xml:lang="fr"><term>Anémie</term>
<term>Biopsie</term>
<term>Compléments alimentaires</term>
<term>Embolisation thérapeutique</term>
<term>Endoscopie gastrointestinale</term>
<term>Entéropathie exsudative</term>
<term>Humains</term>
<term>Indice de gravité médicale</term>
<term>Jeune adulte</term>
<term>Lymphangiectasie intestinale</term>
<term>Lymphoedème</term>
<term>Maladie chronique</term>
<term>Mâle</term>
<term>Procédures de chirurgie digestive</term>
<term>Régime pauvre en graisses</term>
<term>Résultat thérapeutique</term>
</keywords>
</textClass>
</profileDesc>
</teiHeader>
<front><div type="abstract" xml:lang="en">Primary intestinal lymphangiectasia (Waldmann's disease) is a rare disease characterized by dilated lymphatics in the small bowel leading to an exudative enteropathy with lymphopenia, hypoalbuminemia and hypogammaglobulinemia.</div>
</front>
</TEI>
<affiliations><list><country><li>Finlande</li>
<li>Roumanie</li>
</country>
</list>
<tree><country name="Roumanie"><noRegion><name sortKey="Balaban, Vasile Daniel" sort="Balaban, Vasile Daniel" uniqKey="Balaban V" first="Vasile Daniel" last="Balaban">Vasile Daniel Balaban</name>
</noRegion>
<name sortKey="Grasu, Mugur" sort="Grasu, Mugur" uniqKey="Grasu M" first="Mugur" last="Grasu">Mugur Grasu</name>
<name sortKey="Jinga, Mariana" sort="Jinga, Mariana" uniqKey="Jinga M" first="Mariana" last="Jinga">Mariana Jinga</name>
<name sortKey="Vasilescu, Florina" sort="Vasilescu, Florina" uniqKey="Vasilescu F" first="Florina" last="Vasilescu">Florina Vasilescu</name>
</country>
<country name="Finlande"><noRegion><name sortKey="Popp, Alina" sort="Popp, Alina" uniqKey="Popp A" first="Alina" last="Popp">Alina Popp</name>
</noRegion>
</country>
</tree>
</affiliations>
</record>
Pour manipuler ce document sous Unix (Dilib)
EXPLOR_STEP=$WICRI_ROOT/Wicri/Sante/explor/LymphedemaV1/Data/Main/Exploration
HfdSelect -h $EXPLOR_STEP/biblio.hfd -nk 001841 | SxmlIndent | more
Ou
HfdSelect -h $EXPLOR_AREA/Data/Main/Exploration/biblio.hfd -nk 001841 | SxmlIndent | more
Pour mettre un lien sur cette page dans le réseau Wicri
{{Explor lien |wiki= Wicri/Sante |area= LymphedemaV1 |flux= Main |étape= Exploration |type= RBID |clé= pubmed:26405709 |texte= Severe Refractory Anemia in Primary Intestinal Lymphangiectasia. A Case Report. }}
Pour générer des pages wiki
HfdIndexSelect -h $EXPLOR_AREA/Data/Main/Exploration/RBID.i -Sk "pubmed:26405709" \ | HfdSelect -Kh $EXPLOR_AREA/Data/Main/Exploration/biblio.hfd \ | NlmPubMed2Wicri -a LymphedemaV1
This area was generated with Dilib version V0.6.31. |